Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram o...
| Main Authors: | , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Singapore Medical Association
2007
|
| Subjects: | |
| Online Access: | http://irep.iium.edu.my/17108/ http://irep.iium.edu.my/17108/ http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf |
| Summary: | A 39-year-old man was diagnosed with
von Hippel-Lindau syndrome, which was
associated with retinal haemangioblastoma,
cervical cord haemangioblastoma and
bilateral renal cell carcinoma. He subsequently
underwent an arterial embolisation and
cervical laminectomy, following a spinal
angiogram of the cervical lesion. He also
had a right radical nephrectomy, with no
perioperative complications. However, on
admission for the left radical nephrectomy,
he was noted to have preoperative
hypertension. Further investigation
revealed an enlarged left adrenal gland
on abdominal computed tomography
scan and raised urinary catecholamines.
We discuss the risk of renal cell carcinoma
a nd ph a e oc h romoc y toma a r i s ing
concomitantly in von Hippel-Lindau
syndrome, and how best to investigate and
manage them. |
|---|