Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?

A dumbbell-shaped lesion is a solitary tumour that is constricted as it exits the neural foramen. The constriction gives the neurofibroma the appearance of a dumbbell that is used by weight lifters. Neurofibromas that arise from the spinal canal may be intradural or extradural and most commonly in t...

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Main Authors:	Johari, Joehaimey, Omar, Ahmad Sabri, Hau, Mohammad Anwar, Sharifudin, Mohd Ariff
Format:	Conference or Workshop Item
Language:	English English English
Published:	2011
Subjects:	RD701 Orthopedics
Online Access:	http://irep.iium.edu.my/24410/ http://irep.iium.edu.my/24410/1/%28MOA_2011%29_Case_report_of_huge_cervical_dumbbell_tumor_in_neurofibromatosis._Give_up_surgery_%28DrAriff%29.pdf http://irep.iium.edu.my/24410/2/%28MOA_2011%29_Case_report_of_huge_cervical_dumbbell_tumor_in_neurofibromatosis._Give_up_surgery_%28DrAriff%29.pdf http://irep.iium.edu.my/24410/5/case_report_of_a_huge_dumbell_cervical_tumour_in_neurofibromatosis.pdf

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recordtype	eprints
spelling	iium-244102013-02-25T05:24:50Z http://irep.iium.edu.my/24410/ Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery? Johari, Joehaimey Omar, Ahmad Sabri Hau, Mohammad Anwar Sharifudin, Mohd Ariff RD701 Orthopedics A dumbbell-shaped lesion is a solitary tumour that is constricted as it exits the neural foramen. The constriction gives the neurofibroma the appearance of a dumbbell that is used by weight lifters. Neurofibromas that arise from the spinal canal may be intradural or extradural and most commonly in the cervical spine (44%), followed by the thoracic spine (27%) and the lumbar spine (21%). The intraspinal portion of the tumor may cause spinal-cord compression and nerve root failure. The resection of huge dumbbell tumours raises several problems, including preservation of the cervical nerve root, control of the vertebral artery, and maintenance of spine motion, curvature. We report a case of a 14-year-old boy with neurofibromatosis type 1 and intraspinal, extradural tumour of the cervical spine presented with progressive quadriparesis at the level of C3 downward. Surgery was done combined posterior and anterior approach with a 2-stage surgery. The tumour was approached posteriorly in the first surgery, followed by the second surgery from anterior. Duration between the two surgeries was four weeks apart. He showed dramatic recovery immediately following the first surgery and further improved after the second. By the end of two weeks after the second surgery, he was able to manage himself independently, and recovered hi s fine motor functions. Tumour removal by a lateral approach still carries a risk of injuring vital structures. Surgical enucleation of dumbbell cervical tumour in neurofibromatosis gives good prognosis of the recovery despite of the severity of neurology of initial clinical presentation. Two-stage surgery provides safe surgery and minimal morbidity to patient. Technical aspect and advantages are further discussed. 2011 Conference or Workshop Item NonPeerReviewed application/pdf en http://irep.iium.edu.my/24410/1/%28MOA_2011%29_Case_report_of_huge_cervical_dumbbell_tumor_in_neurofibromatosis._Give_up_surgery_%28DrAriff%29.pdf application/pdf en http://irep.iium.edu.my/24410/2/%28MOA_2011%29_Case_report_of_huge_cervical_dumbbell_tumor_in_neurofibromatosis._Give_up_surgery_%28DrAriff%29.pdf application/pdf en http://irep.iium.edu.my/24410/5/case_report_of_a_huge_dumbell_cervical_tumour_in_neurofibromatosis.pdf Johari, Joehaimey and Omar, Ahmad Sabri and Hau, Mohammad Anwar and Sharifudin, Mohd Ariff (2011) Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery? In: 41st Malaysian Orthopaedic Association Annual General Meeting/ Annual Scientific Meeting, 22 - 24 May 2011, Kuala Lumpur Convention Centre. (Unpublished)
repository_type	Digital Repository
institution_category	Local University
institution	International Islamic University Malaysia
building	IIUM Repository
collection	Online Access
language	English English English
topic	RD701 Orthopedics
spellingShingle	RD701 Orthopedics Johari, Joehaimey Omar, Ahmad Sabri Hau, Mohammad Anwar Sharifudin, Mohd Ariff Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?
description	A dumbbell-shaped lesion is a solitary tumour that is constricted as it exits the neural foramen. The constriction gives the neurofibroma the appearance of a dumbbell that is used by weight lifters. Neurofibromas that arise from the spinal canal may be intradural or extradural and most commonly in the cervical spine (44%), followed by the thoracic spine (27%) and the lumbar spine (21%). The intraspinal portion of the tumor may cause spinal-cord compression and nerve root failure. The resection of huge dumbbell tumours raises several problems, including preservation of the cervical nerve root, control of the vertebral artery, and maintenance of spine motion, curvature. We report a case of a 14-year-old boy with neurofibromatosis type 1 and intraspinal, extradural tumour of the cervical spine presented with progressive quadriparesis at the level of C3 downward. Surgery was done combined posterior and anterior approach with a 2-stage surgery. The tumour was approached posteriorly in the first surgery, followed by the second surgery from anterior. Duration between the two surgeries was four weeks apart. He showed dramatic recovery immediately following the first surgery and further improved after the second. By the end of two weeks after the second surgery, he was able to manage himself independently, and recovered hi s fine motor functions. Tumour removal by a lateral approach still carries a risk of injuring vital structures. Surgical enucleation of dumbbell cervical tumour in neurofibromatosis gives good prognosis of the recovery despite of the severity of neurology of initial clinical presentation. Two-stage surgery provides safe surgery and minimal morbidity to patient. Technical aspect and advantages are further discussed.
format	Conference or Workshop Item
author	Johari, Joehaimey Omar, Ahmad Sabri Hau, Mohammad Anwar Sharifudin, Mohd Ariff
author_facet	Johari, Joehaimey Omar, Ahmad Sabri Hau, Mohammad Anwar Sharifudin, Mohd Ariff
author_sort	Johari, Joehaimey
title	Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?
title_short	Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?
title_full	Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?
title_fullStr	Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?
title_full_unstemmed	Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?
title_sort	case report of huge cervical dumbbell tumor in neurofibromatosis. give up surgery?
publishDate	2011
url	http://irep.iium.edu.my/24410/ http://irep.iium.edu.my/24410/1/%28MOA_2011%29_Case_report_of_huge_cervical_dumbbell_tumor_in_neurofibromatosis._Give_up_surgery_%28DrAriff%29.pdf http://irep.iium.edu.my/24410/2/%28MOA_2011%29_Case_report_of_huge_cervical_dumbbell_tumor_in_neurofibromatosis._Give_up_surgery_%28DrAriff%29.pdf http://irep.iium.edu.my/24410/5/case_report_of_a_huge_dumbell_cervical_tumour_in_neurofibromatosis.pdf
first_indexed	2023-09-18T20:36:35Z
last_indexed	2023-09-18T20:36:35Z
_version_	1777409086365630464

Case report of huge cervical dumbbell tumor in neurofibromatosis. Give up surgery?

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