A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal prolife...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
University of Malaya Medical Centre
2006
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| Subjects: | |
| Online Access: | http://irep.iium.edu.my/44330/ http://irep.iium.edu.my/44330/ http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf |
| Summary: | Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that
of fat. |
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